Extramammary Paget''s disease (EMPD) is an unusual neoplasm that affects apocrine gland-bearing skin, such as the vulva, perianal region, scrotum, and penis. However, EMPD has been rarely observed in the non-apocrine, gland-bearing regions; such cases are referred to as “ectopic” EMPD. We present a case involving a 46-year-old man in whom ectopic EMPD affected the scalp. Although the clinical appearance was suggestive of pagetoid Bowen’s disease, EMPD was confirmed by biopsy and immunohistochemical studies. In Korea, there has been only one report of EMPD occurring in the scalp. EMPD of the scalp is extremely rare, with few reported cases. We report a case EMPD of the scalp with a review of the literature