Sarcoidosis can occur as an isolated form or a part of multisystem involvement. Sinonasal involvement in sarcoidosis is rare and the septum and inferior turbinates are most commonly involved. Symptoms are nonspecific and diagnosis of isolated sinonasal sarcoidosis is difficult because it may mimic other sinonasal granulomatous disorders. Exclusion diagnosis is made according to symptoms, laboratory findings, nasal endoscopy, sinus CT, and histopathological features. In this study, we report a case of primary sarcoidosis of the nasal cavity and discuss the clinical characteristics of sinonasal sarcoidosis with a review of literature. (Korean J Otorhinolaryngol-Head Neck Surg 2008;51:938-41) KEY WORDS：Sarcoidosis·Nasal cavity·Granulomatous disease.